![]() ![]() HD is a congenital anomaly that occurs due to a discontinuation of the cranial–caudal migration of neural crest cells, which are responsible for innervation of the colon, or when the ganglion cells undergo premature death between 5th and 12th weeks of pregnancy. The girl was discharged on the 5th day after surgery. Surgical treatment was performed laparoscopically, according to Duhamel-Haddad technique modified with protective loop ileostomy, with good clinical progression. Serology for Chagas’ disease was carried out in order to exclude a diagnosis of Chagas’ Disease megacolon, with negative result. Tests ordered: given the unavailability of barium enema, a computed tomography (CT) study was obtained, revealing the presence of rectal fecaloma ( Figs. The girl refers onset of fecal incontinence at the age of 12. Clinical caseįemale patient, 13 years old, coming from Campo Grande – MS, reports that since birth had intestinal constipation, with mean bowel movements at every 3–5 days with hardened feces, being followed-up by a pediatrician and in treatment for functional constipation. ![]() The infrequency of this diagnosis in this age and the clinical course of this patient underscore the uniqueness of this case. The objective of this paper is to report a case of HD in a 13-old patient, with treatment and outpatient follow-up at the Hospital Regional de Mato Grosso do Sul Rosa Pedrossian – HRMS. In 80% of cases, this disease is diagnosed in the first year of life, being uncommon in adolescence and adulthood such cases usually appear in the form of an ultrashort segment disease. HD presents itself by symptoms of constipation, such as a greater than 48-h delay in elimination of meconium, abdominal distention and vomiting. 3 The distal functional obstruction leads to inefficient peristaltic contractions, with consequent dilatation of proximal intestine, producing megacolon. The absence of ganglion cells results in permanent contraction of the affected segment, preventing the passage of fecal content through that region. ![]() Hirschsprung's Disease (HD), also known as congenital aganglionic megacolon, is an anomaly characterized by an absence of ganglion cells in the myenteric and submucosal plexuses in a variable bowel segment. ![]()
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